Milupa MSUD 2

Milupa MSUD 2 is a powdered medical food containing a mixture of pure L-amino acids free from isoleucine, leucine and valine, and enriched with vitamins, minerals and trace elements. For the dietary management of disorders of branched-chain amino acid metabolism in children and adults, including pregnant women and women of child-bearing age.

MSUD 2 - Main Features

• Isoleucine, leucine and valine-free
• Concentrated, unflavored powder
• Enriched with vitamins, minerals and trace elements
• Osmolality (at a 1 to 9 dilution): 700 mOsm/kg

MSUD 2 - Indications

• Maple syrup urine disease (classic, inherited and intermittent forms)
• Hypervalinemia (isoleucine and leucine should be added)
• Alpha-methylacetoacetic aciduria (leucine and valine should be added)
• Ketotic hypoglycemia (leucine induced, idiopathic form) (isoleucine and valine should be added)
• Hyperprolinemia type II, with hyperleucine-isoleucinemia (valine should be added)

MSUD 2 - Preparation

The amount of MSUD 2 needed to supplement total daily protein requirements (other than isoleucine, leucine and valine) depends on age, body weight and individual tolerance for isoleucine, leucine, and valine. The dose of MSUD 2 must be determined by a physician or dietitian and adjusted periodically. Diets with MSUD 2 must contain adequate amounts of energy, essential fatty acids, isoleucine, leucine and valine to meet daily requirements.

The daily amount required should be divided into 3 to 5 single portions and can be taken mixed with calculated amounts of other food (e.g. beverages, fruit mousse). For accuracy, MSUD 2 should be weighed on a gram scale.

Precaution: Not suitable as a sole source of nutrition. Not for parenteral use.

Storage: Store unopened cans at room temperature. Do not store at extreme temperatures. After opening, keep can tightly covered and store in a cool, dry place (not in the refrigerator) and use within four weeks.

Nutrition Information

MSUD 2 - Ingredients

L-Amino acids (L-Lysine-L-Glutamate, L-Glutamic Acid, L-Proline, L-Aspartic Acid, L-Serine, L-Tyrosine, L-Threonine, L-Phenylalanine, L-Alanine, L-Arginine, Magnesium-L-Aspartate, L-Histidine, L-Methionine, L-Cystine, Glycine, L-Tryptophan), Sugar, Potassium Phosphate, Calcium Phosphate, Calcium Carbonate, Salt, Choline Bitartrate, Myo-Inositol, Ascorbic Acid, Ferrous Sulfate, Vanillin, Niacinamide, Vitamin E Acetate, Zinc Sulfate, Calcium-D-Pantothenate, Copper Acetate, Pyridoxine Hydrochloride, Thiamine Hydrochloride, Riboflavin, Manganese Sulfate, Vitamin A Acetate, Biotin, Folic Acid, Potassium Iodide, Vitamin K1, Ammonium Heptamolybdate, Vitamin D3, Vitamin B12.