XLys, XTrp Maxamum - 454g, Orange flavor

A lysine- and tryptophan-free powdered medical food for the dietary management of glutaric acidemia type I in children over 8 years and adults, including maternal patients.

Main Features:

• Lysine- and tryptophan-free
• Contains a balanced mixture of all other essential and non-essential amino acids, carbohydrate, vitamins, minerals and trace elements
• XLys, XTrp Maxamum provides 40 g of protein equivalent per 100 g of powder
• Pleasant orange flavored powder
• Does not contain fat thereby allowing greater flexibility in modifying energy intake

Indications:

• Glutaric acidemia type I

Preparation:

Maxamum must be consumed in conjunction with natural protein, fluid and other nutrients in quantities prescribed by a physician or dietitian to meet protein and general nutrient requirements.

• The recommended intake of Maxamum will vary depending on the age, bodyweight and medical condition of the individual. Intake should be adjusted to maintain normal growth and development. For accuracy, Maxamum should be weighed on a gram scale. The daily intake of Maxamum should be divided into equal portions and distributed throughout the day.
• Maxamum is best served with meals. Make a paste of the prescribed amount of powder with a small volume of chilled water.
• Gradually add sufficient water to make the desired volume. It is recommended that Maxamum be prepared at a 1 to 7 dilution (e.g. 35 g (approx 1/4 cup) of powder plus 245 mL (approx. 8 fl oz) of water) and advanced to a 1 to 5 dilution (e.g. 35 g (approx 1/4 cup) of powder plus 175 mL (approx. 6 fl oz) of water). These dilutions are guidelines only. Maxamum may be given in a more concentrated form (e.g. drink or paste). If so, water or diluted drinks should be offered at the same time. For best taste, consume immediately. Larger volumes of prepared drink mix should be refrigerated and used within 24 hours or preparation.

Store unopened can at room temperature. Do not store at extreme temperatures. Once opened, reseal can and store in a cool, dry place (not in refrigerator) and use within one month.

XLys, XTrp Maxamum - Ingredients

Sugar, L-Leucine, Corn Syrup Solids, Calcium Phosphate Dibasic, L-Glutamic Acid, L-Proline, L-Arginine, L-Valine, Glycine, L-Isoleucine, L-Aspartic Acid, L-Threonine, Artificial Flavor, L-Phenylalanine, L-Tyrosine, L-Serine, Citric Acid , L-Alanine, L-Histidine, Magnesium Acetate, L-Cystine, Tripotassium Citrate, Choline Bitartrate, Sodium Chloride, L-Methionine, Soy Lecithin, Disodium Hydrogen Phosphate, Dipotassium Hydrogen Phosphate, L-Glutamine, Tricalcium Phosphate, Taurine, L-Ascorbic Acid, M-Inositol, Ferrous Sulfate, L-Carnitine, Zinc Sulfate, DL-Alpha Tocopheryl Acetate, Niacinamide, Manganese Sulfate, Calcium D-Pantothenate, Cupric Sulfate, Pyridoxine Hydrochloride, Sodium Selenite, Thiamine Chloride Hydrochloride, Riboflavin, Vitamin A Acetate, Folic Acid, Artificial Colors (Beta-Carotene, Beet Red), Potassium Iodide, Chromium Chloride, Sodium Molybdate, Phylloquinone, D-Biotin, Vitamin D3, Cyanocobalamin.